Descriptors Found: 1
Displaying: 1 .. 1  

 1 / 1 DeCS     
Descriptor English:   Jaundice, Chronic Idiopathic 
Descriptor Spanish:   Ictericia Idiopática Crónica 
Descriptor Portuguese:   Icterícia Idiopática Crônica 
Synonyms English:   Chronic Idiopathic Jaundice
Chronic Idiopathic Jaundices
Dubin Johnson Syndrome
Dubin-Johnson Syndrome
Hyperbilirubinemia 2
Hyperbilirubinemia 2s
Hyperbilirubinemia II
Hyperbilirubinemia IIs
Idiopathic Jaundice, Chronic
Idiopathic Jaundices, Chronic
Jaundices, Chronic Idiopathic
Syndrome, Dubin-Johnson  
Tree Number:   C16.320.565.300.764
Definition English:   A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract. 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   7735 
Unique Identifier:   D007566 

Occurrence in VHL: