Descriptors Found: 1
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Descriptor English:   Dermatomyositis 
Descriptor Spanish:   Dermatomiositis 
Descriptor Portuguese:   Dermatomiosite 
Synonyms English:   Adult Type Dermatomyositis
Childhood Type Dermatomyositis
Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatomyositis, Juvenile
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile
Polymyositis Dermatomyositis
Tree Number:   C05.651.594.819.500
Definition English:   A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) 
Indexing Annotation English:   coordinate with PARANEOPLASTIC SYNDROMES if pertinent
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   3902 
Unique Identifier:   D003882 

Occurrence in VHL: